구개열을동반한저한성외배엽형성이상환자의 악교정수술을포함한치료: A Clinical report |
김좌영1, 박인영2, 송윤정3 |
1한림대학교강남성심병원 구강악안면외과 2한림대학교성심병원 교정과 3관악서울대학교치과병원 보존과 |
Treatment including orthognathic surgery of a patient with Hypohidrotic ectodermal dysplasia with cleft palate: A Clinical report |
Jwa-Young Kim1, In-Young Park2, Yun-Jung Song3 |
1Department of Oral and Maxillofacial Surgery, Hallym University Kangnam Sacred Heart Hospital 2Department of Orthodontics, Hallym University Sacred Heart Hospital 3Department of Conservative Dentistry, Seoul National University Gwanak Dental Hospital |
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Abstract |
Ectodermal dysplasia is a genetic disorder in which various clinical manifestations involve two or more of the differentiated tissues of the ectoderm. Facial deformity, which is frequently associated with ectodermal dysplasia, appears in the form of cleft lip or cleft palate, especially in the middle facial area.Cleft and tooth defects result in decreased alveolar bone development.This leads to severe skeletal incongruity. Facial features include frontal protrusion, malar bone hypoplasia, flat nose, mandibular prominence and long lower facial height. This clinical report presents treatment including orthognathic surgery of a patient with Hypohidrotic Ectodermal dysplasia with cleft palate. |
Key Words:
Hypohidrotic Ectodermal Dysplasia(HED);orthognathic surgery; |
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